ICD-10-CM
Congenital malformations, deformations and chromosomal abnormalities
Chapter 17, Q00-Q99. CDC FY2027 file dated June 16, 2026.
License: a US government work, in the public domain (Public Domain Mark 1.0).
Categories
87 categories in this chapter. Open one, or page through every code below.
- Q00Anencephaly and similar malformations
- Q01Encephalocele
- Q02Microcephaly
- Q03Congenital hydrocephalus
- Q04Other congenital malformations of brain
- Q05Spina bifida
- Q06Other congenital malformations of spinal cord
- Q07Other congenital malformations of nervous system
- Q10Congenital malform of eyelid, lacrimal apparatus and orbit
- Q11Anophthalmos, microphthalmos and macrophthalmos
- Q12Congenital lens malformations
- Q13Congenital malformations of anterior segment of eye
- Q14Congenital malformations of posterior segment of eye
- Q15Other congenital malformations of eye
- Q16Congenital malform of ear causing impairment of hearing
- Q17Other congenital malformations of ear
- Q18Other congenital malformations of face and neck
- Q20Congenital malformations of cardiac chambers and connections
- Q21Congenital malformations of cardiac septa
- Q22Congenital malformations of pulmonary and tricuspid valves
- Q23Congenital malformations of aortic and mitral valves
- Q24Other congenital malformations of heart
- Q25Congenital malformations of great arteries
- Q26Congenital malformations of great veins
- Q27Other congenital malformations of peripheral vascular system
- Q28Other congenital malformations of circulatory system
- Q30Congenital malformations of nose
- Q31Congenital malformations of larynx
- Q32Congenital malformations of trachea and bronchus
- Q33Congenital malformations of lung
- Q34Other congenital malformations of respiratory system
- Q35Cleft palate
- Q36Cleft lip
- Q37Cleft palate with cleft lip
- Q38Other congenital malformations of tongue, mouth and pharynx
- Q39Congenital malformations of esophagus
51 more categories are in this chapter. Type a code or a term to open one.
Codes
A header groups codes and is not billed. A billable code is one you can report.
321 to 360 of 1,067
- Q40.1Congenital hiatus herniaBillable
- Q40.2Other specified congenital malformations of stomachBillable
- Q40.3Congenital malformation of stomach, unspecifiedBillable
- Q40.8Other congenital malformations of upper alimentary tractBillable
- Q40.9Congenital malformation of upper alimentary tract, unspecifiedBillable
- Q41Congenital absence, atresia and stenosis of small intestineHeader
- Q41.0Congenital absence, atresia and stenosis of duodenumBillable
- Q41.1Congenital absence, atresia and stenosis of jejunumBillable
- Q41.2Congenital absence, atresia and stenosis of ileumBillable
- Q41.8Congenital absence, atresia and stenosis of part sm intBillable
- Q41.9Congen absence, atresia and stenosis of sm int, part unspecifiedBillable
- Q42Congenital absence, atresia and stenosis of large intestineHeader
- Q42.0Congenital absence, atresia and stenosis of rectum with fistulaBillable
- Q42.1Congen absence, atresia and stenosis of rectum without fistulaBillable
- Q42.2Congenital absence, atresia and stenosis of anus with fistulaBillable
- Q42.3Congenital absence, atresia and stenosis of anus without fistulaBillable
- Q42.8Congenital absence, atresia and stenosis of part large intBillable
- Q42.9Congen absence, atresia and stenosis of large int, part unspecifiedBillable
- Q43Other congenital malformations of intestineHeader
- Q43.0Meckel's diverticulum (displaced) (hypertrophic)Billable
- Q43.1Hirschsprung's diseaseBillable
- Q43.2Other congenital functional disorders of colonBillable
- Q43.3Congenital malformations of intestinal fixationBillable
- Q43.4Duplication of intestineBillable
- Q43.5Ectopic anusBillable
- Q43.6Congenital fistula of rectum and anusBillable
- Q43.7Persistent cloacaBillable
- Q43.8Other specified congenital malformations of intestineBillable
- Q43.9Congenital malformation of intestine, unspecifiedBillable
- Q44Congenital malform of gallbladder, bile ducts and liverHeader
- Q44.0Agenesis, aplasia and hypoplasia of gallbladderBillable
- Q44.1Other congenital malformations of gallbladderBillable
- Q44.2Atresia of bile ductsBillable
- Q44.3Congenital stenosis and stricture of bile ductsBillable
- Q44.4Choledochal cystBillable
- Q44.5Other congenital malformations of bile ductsBillable
- Q44.6Cystic disease of liverBillable
- Q44.7Other congenital malformations of liverHeader
- Q44.70Other congenital malformation of liver, unspecifiedBillable
- Q44.71Alagille syndromeBillable
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