ICD-10-CM
ICD-10 code for Alagille syndrome: Q44.71
The closest CDC title for "Alagille syndrome" is Q44.71, Alagille syndrome. Q44.71 is a billable code.
Source: CDC ICD-10-CM FY2027 order file dated June 16, 2026. Publisher page
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Codes under Q44, then other CDC titles that name alagille syndrome
A header groups codes and is not billed. A billable code is one you can report.
- Q44Congenital malformations of gallbladder, bile ducts and liverHeader
- Q44.0Agenesis, aplasia and hypoplasia of gallbladderBillable
- Q44.1Other congenital malformations of gallbladderBillable
- Q44.2Atresia of bile ductsBillable
- Q44.3Congenital stenosis and stricture of bile ductsBillable
- Q44.4Choledochal cystBillable
- Q44.5Other congenital malformations of bile ductsBillable
- Q44.6Cystic disease of liverBillable
- Q44.7Other congenital malformations of liverHeader
- Q44.70Other congenital malformation of liver, unspecifiedBillable
- Q44.71Alagille syndromeBillable
- Q44.79Other congenital malformations of liverBillable
Code also
The CDC tabular list says a second code may be needed with this one. The note does not set which is listed first.
From Q44.7. A note on a category applies to every code under it.
Code also, if applicable, associated malformations affecting other systems
Related pages
- Q44.71 code detailsNotes, nearby codes, CMS-HCC group
- Category Q44Every code under it
- Chapter 17Congenital malformations and chromosomal abnormalities
- ICD-10 codes by conditionA to Z
- Check a list of ICD-10 codes
- Denial code CO-11Diagnosis does not support the procedure
- Denial code CO-146Diagnosis invalid for the date of service
- HCPCS Level II code lookup
Questions
What is the ICD-10 code for Alagille syndrome?
The closest CDC title for "Alagille syndrome" is Q44.71, Alagille syndrome. Q44.71 is a billable code.
Is Q44.71 billable?
Yes. Q44.71 is a billable code in the FY2027 ICD-10-CM file. Use a more specific code when the record documents one.
What chapter is Q44.71 in?
Chapter 17. Congenital malformations and chromosomal abnormalities.
When do ICD-10-CM codes change?
Every October 1, with the new fiscal year file. Some years add April 1 updates. This page uses the FY2027 file, effective October 1, 2026.