ICD-10-CM
ICD-10 code for Disorder (of) propionic acidemia: E71.121
The ICD-10-CM index points "Disorder (of) propionic acidemia" to E71.121, Propionic acidemia. E71.121 is a billable code.
Source: CDC ICD-10-CM FY2027 Alphabetic Index file dated June 16, 2026. Publisher page
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More specific codes in E71
A header groups codes and is not billed. A billable code is one you can report.
- E71Disorders of branched-chain amino-acid metabolism and fatty-acid metabolismHeader
- E71.0Maple-syrup-urine diseaseBillable
- E71.1Other disorders of branched-chain amino-acid metabolismHeader
- E71.11Branched-chain organic aciduriasHeader
- E71.110Isovaleric acidemiaBillable
- E71.1113-methylglutaconic aciduriaBillable
- E71.118Other branched-chain organic aciduriasBillable
- E71.12Disorders of propionate metabolismHeader
- E71.120Methylmalonic acidemiaBillable
- E71.121Propionic acidemiaBillable
- E71.128Other disorders of propionate metabolismBillable
- E71.19Other disorders of branched-chain amino-acid metabolismBillable
- E71.2Disorder of branched-chain amino-acid metabolism, unspecifiedBillable
- E71.3Disorders of fatty-acid metabolismHeader
- E71.30Disorder of fatty-acid metabolism, unspecifiedBillable
- E71.31Disorders of fatty-acid oxidationHeader
- E71.310Long chain/very long chain acyl CoA dehydrogenase deficiencyBillable
- E71.311Medium chain acyl CoA dehydrogenase deficiencyBillable
- E71.312Short chain acyl CoA dehydrogenase deficiencyBillable
- E71.313Glutaric aciduria type IIBillable
- E71.314Muscle carnitine palmitoyltransferase deficiencyBillable
- E71.318Other disorders of fatty-acid oxidationBillable
- E71.32Disorders of ketone metabolismBillable
- E71.39Other disorders of fatty-acid metabolismBillable
- E71.4Disorders of carnitine metabolismHeader
- E71.40Disorder of carnitine metabolism, unspecifiedBillable
- E71.41Primary carnitine deficiencyBillable
- E71.42Carnitine deficiency due to inborn errors of metabolismBillable
- E71.43Iatrogenic carnitine deficiencyBillable
- E71.44Other secondary carnitine deficiencyHeader
- E71.440Ruvalcaba-Myhre-Smith syndromeBillable
- E71.448Other secondary carnitine deficiencyBillable
- E71.5Peroxisomal disordersHeader
- E71.50Peroxisomal disorder, unspecifiedBillable
- E71.51Disorders of peroxisome biogenesisHeader
- E71.510Zellweger syndromeBillable
- E71.511Neonatal adrenoleukodystrophyBillable
- E71.518Other disorders of peroxisome biogenesisBillable
- E71.52X-linked adrenoleukodystrophyHeader
- E71.520Childhood cerebral X-linked adrenoleukodystrophyBillable
- E71.521Adolescent X-linked adrenoleukodystrophyBillable
- E71.522AdrenomyeloneuropathyBillable
- E71.528Other X-linked adrenoleukodystrophyBillable
- E71.529X-linked adrenoleukodystrophy, unspecified typeBillable
- E71.53Other group 2 peroxisomal disordersBillable
- E71.54Other peroxisomal disordersHeader
- E71.540Rhizomelic chondrodysplasia punctataBillable
- E71.541Zellweger-like syndromeBillable
- E71.542Other group 3 peroxisomal disordersBillable
- E71.548Other peroxisomal disordersBillable
Related conditions
Related pages
- E71.121 code detailsNotes, nearby codes, CMS-HCC group
- Category E71Every code under it
- Chapter 4Endocrine, nutritional and metabolic diseases
- ICD-10 codes by conditionA to Z
- Check a list of ICD-10 codes
- Denial code CO-11Diagnosis does not support the procedure
- Denial code CO-146Diagnosis invalid for the date of service
- HCPCS Level II code lookup
Questions
What is the ICD-10 code for Disorder (of) propionic acidemia?
The ICD-10-CM index points "Disorder (of) propionic acidemia" to E71.121, Propionic acidemia. E71.121 is a billable code.
Is E71.121 billable?
Yes. E71.121 is a billable code in the FY2027 ICD-10-CM file. Use a more specific code when the record documents one.
What chapter is E71.121 in?
Chapter 4. Endocrine, nutritional and metabolic diseases.
When do ICD-10-CM codes change?
Every October 1, with the new fiscal year file. Some years add April 1 updates. This page uses the FY2027 file, effective October 1, 2026.