ICD-10-CM
ICD-10 code for Lymphohistiocytosis: D76.1
The closest CDC title for "Lymphohistiocytosis" is D76.1, Hemophagocytic lymphohistiocytosis. D76.1 is a billable code.
Source: CDC ICD-10-CM FY2027 order file dated June 16, 2026. Publisher page
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Codes under D76, then other CDC titles that name hemophagocytic lymphohistiocytosis
A header groups codes and is not billed. A billable code is one you can report.
Excludes1
Excludes1 means these codes are not reported together.
From D76. A note on a category applies to every code under it.
- C96.0(Abt-) Letterer-Siwe disease
- C96.6Eosinophilic granuloma
- C96.5Hand-Schüller-Christian disease
- C96.9Histiocytic medullary reticulosis
- C96.AHistiocytic sarcoma
- C96.5Histiocytosis X, multifocal
- C96.6Histiocytosis X, unifocal
- C96.5Langerhans-cell histiocytosis, multifocal
- C96.6Langerhans-cell histiocytosis NOS
- C96.6Langerhans-cell histiocytosis, unifocal
- C91.4-Leukemic reticuloendotheliosis
- I89.8Lipomelanotic reticulosis
- C96.AMalignant histiocytosis
- C86.0Malignant reticulosis
- C96.0Nonlipid reticuloendotheliosis
Related conditions
Related pages
- D76.1 code detailsNotes, nearby codes, CMS-HCC group
- Category D76Every code under it
- Chapter 3Diseases of the blood and blood-forming organs
- ICD-10 codes by conditionA to Z
- Check a list of ICD-10 codes
- Denial code CO-11Diagnosis does not support the procedure
- Denial code CO-146Diagnosis invalid for the date of service
- HCPCS Level II code lookup
Questions
What is the ICD-10 code for Lymphohistiocytosis?
The closest CDC title for "Lymphohistiocytosis" is D76.1, Hemophagocytic lymphohistiocytosis. D76.1 is a billable code.
Is D76.1 billable?
Yes. D76.1 is a billable code in the FY2027 ICD-10-CM file. Use a more specific code when the record documents one.
What documentation notes apply to D76.1?
The CDC tabular list gives 15 Excludes1 notes (not coded together) for D76.1 and the categories above it. They are listed on this page.
What chapter is D76.1 in?
Chapter 3. Diseases of the blood and blood-forming organs.
When do ICD-10-CM codes change?
Every October 1, with the new fiscal year file. Some years add April 1 updates. This page uses the FY2027 file, effective October 1, 2026.