ICD-10-CM
ICD-10 code for Syndrome Ruvalcaba-Myhre-Smith: E71.440
The ICD-10-CM index points "Syndrome Ruvalcaba-Myhre-Smith" to E71.440, Ruvalcaba-Myhre-Smith syndrome. E71.440 is a billable code.
Source: CDC ICD-10-CM FY2027 Alphabetic Index file dated June 16, 2026. Publisher page
Run it in Rivvi
Check every code on your export
Upload a claims or problem-list export. Rivvi flags codes that are not billable, replaced, or unspecified when a specific code exists.
Check my exportFree to start. Opens Rivvi, the AI workspace for healthcare teams.
More specific codes in E71
A header groups codes and is not billed. A billable code is one you can report.
- E71Disorders of branched-chain amino-acid metabolism and fatty-acid metabolismHeader
- E71.0Maple-syrup-urine diseaseBillable
- E71.1Other disorders of branched-chain amino-acid metabolismHeader
- E71.11Branched-chain organic aciduriasHeader
- E71.110Isovaleric acidemiaBillable
- E71.1113-methylglutaconic aciduriaBillable
- E71.118Other branched-chain organic aciduriasBillable
- E71.12Disorders of propionate metabolismHeader
- E71.120Methylmalonic acidemiaBillable
- E71.121Propionic acidemiaBillable
- E71.128Other disorders of propionate metabolismBillable
- E71.19Other disorders of branched-chain amino-acid metabolismBillable
- E71.2Disorder of branched-chain amino-acid metabolism, unspecifiedBillable
- E71.3Disorders of fatty-acid metabolismHeader
- E71.30Disorder of fatty-acid metabolism, unspecifiedBillable
- E71.31Disorders of fatty-acid oxidationHeader
- E71.310Long chain/very long chain acyl CoA dehydrogenase deficiencyBillable
- E71.311Medium chain acyl CoA dehydrogenase deficiencyBillable
- E71.312Short chain acyl CoA dehydrogenase deficiencyBillable
- E71.313Glutaric aciduria type IIBillable
- E71.314Muscle carnitine palmitoyltransferase deficiencyBillable
- E71.318Other disorders of fatty-acid oxidationBillable
- E71.32Disorders of ketone metabolismBillable
- E71.39Other disorders of fatty-acid metabolismBillable
- E71.4Disorders of carnitine metabolismHeader
- E71.40Disorder of carnitine metabolism, unspecifiedBillable
- E71.41Primary carnitine deficiencyBillable
- E71.42Carnitine deficiency due to inborn errors of metabolismBillable
- E71.43Iatrogenic carnitine deficiencyBillable
- E71.44Other secondary carnitine deficiencyHeader
- E71.440Ruvalcaba-Myhre-Smith syndromeBillable
- E71.448Other secondary carnitine deficiencyBillable
- E71.5Peroxisomal disordersHeader
- E71.50Peroxisomal disorder, unspecifiedBillable
- E71.51Disorders of peroxisome biogenesisHeader
- E71.510Zellweger syndromeBillable
- E71.511Neonatal adrenoleukodystrophyBillable
- E71.518Other disorders of peroxisome biogenesisBillable
- E71.52X-linked adrenoleukodystrophyHeader
- E71.520Childhood cerebral X-linked adrenoleukodystrophyBillable
- E71.521Adolescent X-linked adrenoleukodystrophyBillable
- E71.522AdrenomyeloneuropathyBillable
- E71.528Other X-linked adrenoleukodystrophyBillable
- E71.529X-linked adrenoleukodystrophy, unspecified typeBillable
- E71.53Other group 2 peroxisomal disordersBillable
- E71.54Other peroxisomal disordersHeader
- E71.540Rhizomelic chondrodysplasia punctataBillable
- E71.541Zellweger-like syndromeBillable
- E71.542Other group 3 peroxisomal disordersBillable
- E71.548Other peroxisomal disordersBillable
Excludes1
Excludes1 means these codes are not reported together.
From E71.4. A note on a category applies to every code under it.
Related conditions
Related pages
- E71.440 code detailsNotes, nearby codes, CMS-HCC group
- Category E71Every code under it
- Chapter 4Endocrine, nutritional and metabolic diseases
- ICD-10 codes by conditionA to Z
- Check a list of ICD-10 codes
- Denial code CO-11Diagnosis does not support the procedure
- Denial code CO-146Diagnosis invalid for the date of service
- HCPCS Level II code lookup
Questions
What is the ICD-10 code for Syndrome Ruvalcaba-Myhre-Smith?
The ICD-10-CM index points "Syndrome Ruvalcaba-Myhre-Smith" to E71.440, Ruvalcaba-Myhre-Smith syndrome. E71.440 is a billable code.
Is E71.440 billable?
Yes. E71.440 is a billable code in the FY2027 ICD-10-CM file. Use a more specific code when the record documents one.
What documentation notes apply to E71.440?
The CDC tabular list gives 1 Excludes1 note (not coded together) for E71.440 and the categories above it. They are listed on this page.
What chapter is E71.440 in?
Chapter 4. Endocrine, nutritional and metabolic diseases.
When do ICD-10-CM codes change?
Every October 1, with the new fiscal year file. Some years add April 1 updates. This page uses the FY2027 file, effective October 1, 2026.