ICD-10-CM
ICD-10 code for Usher syndrome: Q99.819
The CDC title for "Usher syndrome" is Q99.81 (Usher syndrome), a header that is not billable. When nothing more specific is documented, the billable code is Q99.819, Usher syndrome, unspecified.
Source: CDC ICD-10-CM FY2027 order file dated June 16, 2026. Publisher page
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Codes under Q99.81, then other CDC titles that name usher syndrome
A header groups codes and is not billed. A billable code is one you can report.
Use additional code
The CDC tabular list says to add the code named here after this one when it applies.
From Q99.81. A note on a category applies to every code under it.
Use additional code to identify any auditory and visual manifestations
Related conditions
Related pages
- Q99.819 code detailsNotes, nearby codes, CMS-HCC group
- Category Q99.81Every code under it
- Chapter 17Congenital malformations and chromosomal abnormalities
- ICD-10 codes by conditionA to Z
- Check a list of ICD-10 codes
- Denial code CO-11Diagnosis does not support the procedure
- Denial code CO-146Diagnosis invalid for the date of service
- HCPCS Level II code lookup
Questions
What is the ICD-10 code for Usher syndrome?
The CDC title for "Usher syndrome" is Q99.81 (Usher syndrome), a header that is not billable. When nothing more specific is documented, the billable code is Q99.819, Usher syndrome, unspecified.
Is Q99.819 billable?
Yes. Q99.819 is a billable code in the FY2027 ICD-10-CM file. Use a more specific code when the record documents one.
What documentation notes apply to Q99.819?
The CDC tabular list gives 1 "use additional code" note for Q99.819 and the categories above it. They are listed on this page.
What chapter is Q99.819 in?
Chapter 17. Congenital malformations and chromosomal abnormalities.
When do ICD-10-CM codes change?
Every October 1, with the new fiscal year file. Some years add April 1 updates. This page uses the FY2027 file, effective October 1, 2026.