ICD-10-CM
ICD-10 code for VEXAS syndrome: M04.3
The closest CDC title for "VEXAS syndrome" is M04.3, VEXAS syndrome. M04.3 is a billable code.
Source: CDC ICD-10-CM FY2027 order file dated June 16, 2026. Publisher page
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Codes under M04, then other CDC titles that name vexas syndrome
A header groups codes and is not billed. A billable code is one you can report.
Code also
The CDC tabular list says a second code may be needed with this one. The note does not set which is listed first.
Code also any associated conditions
Excludes2
Excludes2 means the other condition can be reported with this one when both are documented.
From M04. A note on a category applies to every code under it.
Related conditions
Related pages
- M04.3 code detailsNotes, nearby codes, CMS-HCC group
- Category M04Every code under it
- Chapter 13Diseases of the musculoskeletal system
- ICD-10 codes by conditionA to Z
- Check a list of ICD-10 codes
- Denial code CO-11Diagnosis does not support the procedure
- Denial code CO-146Diagnosis invalid for the date of service
- HCPCS Level II code lookup
Questions
What is the ICD-10 code for VEXAS syndrome?
The closest CDC title for "VEXAS syndrome" is M04.3, VEXAS syndrome. M04.3 is a billable code.
Is M04.3 billable?
Yes. M04.3 is a billable code in the FY2027 ICD-10-CM file. Use a more specific code when the record documents one.
What documentation notes apply to M04.3?
The CDC tabular list gives 1 Excludes2 note (may be coded together when both are documented) for M04.3 and the categories above it. They are listed on this page.
What chapter is M04.3 in?
Chapter 13. Diseases of the musculoskeletal system.
When do ICD-10-CM codes change?
Every October 1, with the new fiscal year file. Some years add April 1 updates. This page uses the FY2027 file, effective October 1, 2026.