ICD-10-CM
Congenital malformations, deformations and chromosomal abnormalities
Chapter 17, Q00-Q99. CDC FY2027 file dated June 16, 2026.
License: a US government work, in the public domain (Public Domain Mark 1.0).
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Categories
87 categories in this chapter. Open one, or page through every code below.
- Q00Anencephaly and similar malformations
- Q01Encephalocele
- Q02Microcephaly
- Q03Congenital hydrocephalus
- Q04Other congenital malformations of brain
- Q05Spina bifida
- Q06Other congenital malformations of spinal cord
- Q07Other congenital malformations of nervous system
- Q10Congenital malform of eyelid, lacrimal apparatus and orbit
- Q11Anophthalmos, microphthalmos and macrophthalmos
- Q12Congenital lens malformations
- Q13Congenital malformations of anterior segment of eye
- Q14Congenital malformations of posterior segment of eye
- Q15Other congenital malformations of eye
- Q16Congenital malform of ear causing impairment of hearing
- Q17Other congenital malformations of ear
- Q18Other congenital malformations of face and neck
- Q20Congenital malformations of cardiac chambers and connections
- Q21Congenital malformations of cardiac septa
- Q22Congenital malformations of pulmonary and tricuspid valves
- Q23Congenital malformations of aortic and mitral valves
- Q24Other congenital malformations of heart
- Q25Congenital malformations of great arteries
- Q26Congenital malformations of great veins
- Q27Other congenital malformations of peripheral vascular system
- Q28Other congenital malformations of circulatory system
- Q30Congenital malformations of nose
- Q31Congenital malformations of larynx
- Q32Congenital malformations of trachea and bronchus
- Q33Congenital malformations of lung
- Q34Other congenital malformations of respiratory system
- Q35Cleft palate
- Q36Cleft lip
- Q37Cleft palate with cleft lip
- Q38Other congenital malformations of tongue, mouth and pharynx
- Q39Congenital malformations of esophagus
51 more categories are in this chapter. Type a code or a term to open one.
Codes
A header groups codes and is not billed. A billable code is one you can report.
801 to 840 of 1,067
- Q75.03Metopic craniosynostosisBillable
- Q75.04Lambdoid craniosynostosisHeader
- Q75.041Lambdoid craniosynostosis, unilateralBillable
- Q75.042Lambdoid craniosynostosis, bilateralBillable
- Q75.049Lambdoid craniosynostosis, unspecifiedBillable
- Q75.05Multi-suture craniosynostosisHeader
- Q75.051Cloverleaf skullBillable
- Q75.052PansynostosisBillable
- Q75.058Other multi-suture craniosynostosisBillable
- Q75.08Other single-suture craniosynostosisBillable
- Q75.1Craniofacial dysostosisBillable
- Q75.2HypertelorismBillable
- Q75.3MacrocephalyBillable
- Q75.4Mandibulofacial dysostosisBillable
- Q75.5Oculomandibular dysostosisBillable
- Q75.8Other congenital malformations of skull and face bonesBillable
- Q75.9Congenital malformation of skull and face bones, unspecifiedBillable
- Q76Congenital malformations of spine and bony thoraxHeader
- Q76.0Spina bifida occultaBillable
- Q76.1Klippel-Feil syndromeBillable
- Q76.2Congenital spondylolisthesisBillable
- Q76.3Congenital scoliosis due to congenital bony malformationBillable
- Q76.4Other congenital malform of spine, not associated with scoliosisHeader
- Q76.41Congenital kyphosisHeader
- Q76.411Congenital kyphosis, occipito-atlanto-axial regionBillable
- Q76.412Congenital kyphosis, cervical regionBillable
- Q76.413Congenital kyphosis, cervicothoracic regionBillable
- Q76.414Congenital kyphosis, thoracic regionBillable
- Q76.415Congenital kyphosis, thoracolumbar regionBillable
- Q76.419Congenital kyphosis, unspecified regionBillable
- Q76.42Congenital lordosisHeader
- Q76.425Congenital lordosis, thoracolumbar regionBillable
- Q76.426Congenital lordosis, lumbar regionBillable
- Q76.427Congenital lordosis, lumbosacral regionBillable
- Q76.428Congenital lordosis, sacral and sacrococcygeal regionBillable
- Q76.429Congenital lordosis, unspecified regionBillable
- Q76.49Other congenital malform of spine, not associated with scoliosisBillable
- Q76.5Cervical ribBillable
- Q76.6Other congenital malformations of ribsBillable
- Q76.7Congenital malformation of sternumBillable